Domain | Activity level | Description |
---|---|---|
Biological | No=0 | Absence of any of the following biological feature |
Low=1 | Clonal component and/or hypocomplementemia (low C4 or C3 or CH50) and/or hypergammaglobulinemia or high IgG level between 16 and 20 g/L | |
Moderate=2 | Presence of cryoglobulinemia and/or hypergammaglobulinemia or high IgG level >20 g/L, and/or recent onset hypogammaglobulinemia or recent decrease of IgG level (<5 g/L) |