Table 1

Types of autoimmune diseases in relatives of IgG4-RD patients

Family history of AIDNumber of IgG4-RD patients (n=93)Percentage (%)
RA3436.6
IgG4-RD1617.2
SLE88.6
Psoriasis88.6
GD88.6
HT77.5
SS66.4
Spondyloarthritis66.4
Vitiligo33.2
PBC33.2
DM22.2
Autoimmune nephritis22.2
ITP22.2
UCTD11.1
Type1 diabetes11.1
AIH11.1
TA11.1
AIHA11.1
  • AIH, autoimmune hepatitis; AIHA, autoimmune haemolytic anaemia; DM, dermatomyositis; GD, Grave’s disease; HT, Hashimoto thyroiditis; IgG4-RD, IgG4-related disease; ITP, immune thrombocytopenia; PBC, primary biliary cholangitis; RA, rheumatoid arthritis; SLE, systemic lupus erythematosus; SS, Sjögren’s syndrome; TA, Takayasu arteritis; UCTD, undifferentiated connective tissue disease.