Autoimmune diseases (AID) in patients presenting an episode of invasive fungal disease (IFD)
| Pneumocystis pneumonia (227) | Fungemia (167) | Invasive aspergillosis (84) | Other IFD (58) | Multiple IFD (13) | Total (549) | |
| Rheumatoid arthritis | 55 (24.2) | 28 (16.8) | 15 (17.9) | 13 (22.4) | 2 (15) | 113 (20.6) |
| Inflammatory bowel disease (IBD) | 13 (5.7) | 36 (21.6) | 2 (2.4) | 3 (5.2) | 0 (0) | 54 (9.8) |
| Crohn’s disease | 9 (4.0) | 29 (17.4) | 2 (2.4) | 2 (3.4) | 0 (0) | 42 (7.7) |
| Ulcerative colitis | 4 (1.8) | 6 (3.6) | 0 (0) | 1 (1.7) | 0 (0) | 11 (2.0) |
| Unclassified IBD | 0 (0) | 1 (0.6) | 0 (0) | 0 (0) | 0 (0) | 1 (0.2) |
| Sarcoidosis | 19 (8.4) | 10 (6.0) | 10 (11.9) | 6 (10.3) | 1 (8) | 46 (8.4) |
| ANCA-associated vasculitis | 25 (11.0) | 7 (4.2) | 10 (11.9) | 2 (3.4) | 2 (15) | 46 (8.4) |
| Granulomatosis with polyangiitis | 11 (4.8) | 4 (2.4) | 5 (6.0) | 0 (0) | 0 (0) | 20 (3.6) |
| Microscopic polyangiitis | 11 (4.8) | 1 (0.6) | 5 (6.0) | 0 (0) | 1 (8) | 18 (3.3) |
| Eosinophilic granulomatosis with polyangiitis | 1 (0.4) | 2 (1.2) | 0 (0) | 2 (3.4) | 0 (0) | 5 (0.9) |
| Unclassified ANCA-associated vasculitis | 2 (0.9) | 0 (0) | 0 (0) | 0 (0) | 1 (8) | 3 (0.5) |
| Systemic lupus erythematosus | 6 (2.6) | 12 (7.2) | 9 (10.7) | 7 (12.1) | 2 (15) | 36 (6.6) |
| Dermatomyositis | 21 (9.3) | 7 (4.2) | 1 (1.2) | 4 (6.9) | 0 (0) | 33 (6) |
| Systemic sclerosis | 12 (5.3) | 12 (7.2) | 1 (1.2) | 3 (5.2) | 0 (0) | 28 (5.1) |
| Giant-cell arteritis | 11 (4.8) | 0 (0) | 1 (1.2) | 4 (6.9) | 0 (0) | 16 (2.9) |
| Spondylarthritis | 2 (0.9) | 4 (2.4) | 7 (8.3) | 3 (5.2) | 0 (0) | 16 (2.9) |
| Sjögren’s syndrome | 7 (3.1) | 4 (2.4) | 1 (1.2) | 2 (3.4) | 0 (0) | 14 (2.6) |
| Autoimmune hepatitis | 0 (0) | 6 (3.6) | 2 (2.4) | 1 (1.7) | 2 (15) | 11 (2.0) |
| Polymyalgia rheumatica | 5 (2.2) | 3 (1.8) | 1 (1.2) | 1 (1.7) | 0 (0) | 10 (1.8) |
| Autoimmune haemolytic anaemia | 5 (2.2) | 2 (1.2) | 0 (0) | 2 (3.4) | 0 (0) | 9 (1.6) |
| Myasthenia gravis | 4 (1.8) | 1 (0.6) | 2 (2.4) | 1 (1.7) | 0 (0) | 8 (1.5) |
| Multiple sclerosis | 0 (0) | 7 (4.2) | 1 (1.2) | 0 (0) | 0 (0) | 8 (1.5) |
| Psoriasis | 4 (1.8) | 0 (0) | 3 (3.6) | 0 (0) | 0 (0) | 7 (1.3) |
| Psoriatic arthritis | 5 (2.2) | 0 (0) | 2 (2.4) | 0 (0) | 0 (0) | 7 (1.3) |
| Immune thrombocytopenic purpura | 4 (1.8) | 1 (0.6) | 1 (1.2) | 0 (0) | 0 (0) | 6 (1.1) |
| Other | 29 (12.8) | 27 (16.2) | 15 (17.9) | 6 (10.3) | 4 (31) | 81 (14.8) |
Results are presented as n (%); only one AID per patient reported: 82 patients had at least two concomitant AIDs (most frequent combination: rheumatoid arthritis and Sjögren’s syndrome in 9 patients), 10 had three concomitant AIDs (further details in online supplemental table S9).